Orphanet: Syndrome congenital d hamartome hypothalamique. Request PDF on ResearchGate | On Jul 1, , J. Mounach and others published Puberté précoce liée à un hamartome hypothalamique. Request PDF on ResearchGate | On May 1, , N. Ech-Cherif El Kettani and others published Hamartome hypothalamique révélant des crises gélastiques.

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Published online May 1. These classifications have been accomplished according to the symptomatology and the feasibility of treatment modalities Fig. Hypohalamique Center for Biotechnology InformationU.

The relationship between magnetic resonance imaging findings and clinical manifestations of hypothalamic hamartoma. Access to the text HTML.

Translation of “hypothalamus hamartome” in English

This syndrome disappeared spontaneously within 10 days 8. Access to the PDF text. An immediate seizure-free condition was the single most reliable factor for long-term seizure outcome. Access to the full text of this article requires a subscription. A peel-away catheter is then replaced via the tract. An optimal surgical approach should be selected based on the individual status of the lesion and the patient Fig. Le syndrome hamartome hypothalamique: Careful planning and a stepwise approach with the advanced surgical technique will make it possible 24 A proper trajectory directly to HHs and keeping the disconnection margin straight are essential instructions for minimizing complications.

The disconnection will begin at the border between the hamartomas and the mammillary body and proceed along the midline posteroinferior hypothalamiwue of the third ventricle Fig.

hypothalamus hamartome – Translation into English – examples French | Reverso Context

The presence of these neurons constitute relevant evidence for ictogenesis of HH 3918 Personal information regarding our website’s visitors, including their identity, is confidential. CT, MR, and pathologic findings.


Electrophysiological properties of human hypothalamic hamartomas. Ictal laughter associated with paroxysmal hypothalamopituitary dysfunction.

Transendoscopic intraoperative recording of gelastic seizures from a hypothalamic hamartoma. You can move this window by clicking on the headline. High frequency stimulation of the mamillothalamic tract for the treatment of resistant seizures associated with hypothalamic hamartoma.

Villeneuve abV. If you are a subscriber, please sign in ‘My Account’ at the top right of the screen. Acute intralesional recording in hypothalamic hamartoma: Laguitton aM. After confirmation of the extent of disconnection and seizure outcome, a second hamqrtome can be performed with fewer complications. Neurosurg Clin N Am. This activating network results in epileptic discharges through the premotor and frontal opercular areas voluntary systemwhich are located on the same side of the broader attachment Advances and Technical Standards in Neurosurgery.

Classification and possible treatment selection for hypothalamic hamartoma HH modification from Choi et al. Presurgical evaluation is very much the same as a phase 1 study for a medically intractable epilepsy patient. You may thus request that your data, should it be inaccurate, incomplete, unclear, outdated, not be used or stored, be corrected, clarified, updated or deleted.

Disconnection of HHs from the hypothalamus with a monopolar coagulator. J Neurol Neurosurg Psychiatry. Most epileptiform discharges arise from the broad attachment side 31 Compulsive bursts of laughter are a typical and classical feature of GS 13 However, surgical resection for total removal of Hamarto,e have led to good seizure outcomes and behavioral improvement 10 Surgical outcomes Hypothalamisue et al.

The confines of the protruding hamartoma and the normal hypothalamus can be easily determined by direct visualization; however, for difficult cases, the depth electrode is hypofhalamique prior to endoscopic surgery to guide the depth and the margin of disconnection.

Personal information regarding our website’s visitors, including their identity, is confidential. Hypothalamic hamartoma with refractory epilepsy: The mass should not be under the optic tract. EEG and video-EEG seizure monitoring has limited utility in patients with hypothalamic hamartoma and hypotjalamique.

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Endoscopic surgery for hypothalamic hamartomas causing medically refractory gelastic epilepsy. Due to its nature of generating hypothalamiqud discharge and spreading to cortical region, various management strategies have been proposed and combined. Clear visualization of a distinct cleft or indentation and the border connecting HH to the hypothalamus will be the critical point for performing staged endoscopic disconnection for giant HHs.

Because breaking down the tract for spreading epileptiform discharge from HHs to the frontotemporal cortical region will be the optimal solution for this lesion, further aggressive maneuvers may not be necessary 19 Utility of early single photon emission computed tomography SPECT in neonatal gelastic epilepsy associated with hypothalamic hamartoma.

Because these patients are mostly clinically and socially impaired, pursuing resection or disconnection would be more beneficial for these patients This rare non-neoplastic abnormal mixture of neuronal and glial tissue hanartome the inferior hypothalamus has been postulated to be derived from the mammillo-thalamo-cingulate tract from which HH is networking other brain areas associated with GS or the pathway from the HH to the brainstem and cerebellum 16 As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that lawaccess art 34 of that law and rectify art 36 of that law your personal data.

Access to the full text of this article requires a subscription. Baizri cH.